Amelogenesis Imperfecta: A Case Report and Review of Literature

Pankhuri Nigam; Vijay Pal Singh; Krishna Deo Prasad; Jalaj Tak

Pankhuri Nigam Post-graduate Student, Department of Oral & Maxillofacial Pathology and Microbiology
Vijay Pal Singh Post-graduate Student, Department of Orthodontics and Dentofacial Orthopaedics
Krishna Deo Prasad Professor and Head, Department of Oral & Maxillofacial Pathology and Microbiology
Jalaj Tak Reader,Department of Oral & Maxillofacial Pathology and Microbiology

Keywords: Amelogenesis imperfecta, Enamel, Hereditary, Management, Treatment

Abstract

Amelogenesis imperfecta (AI) is a hereditary disorder that causes developmental alterations in the structure of enamel. It
represents a group of heterogenous conditions. AI has several names such as hereditary enamel dysplasia, hereditary brown
enamel, hereditary brown opalescent teeth. In this disorder, the enamel is hypoplastic, hypomineralized or both. It may show
autosomal dominant, autosomal recessive, sex-linked or sporadic pattern. It is necessary to diagnose this disorder and provide
durable, functional and esthetic management of these patients to improve the quality of their lives. We present a case of AI
affecting the dentition of an 18-year-old girl.

Author Biographies

Pankhuri Nigam, Post-graduate Student, Department of Oral & Maxillofacial Pathology and Microbiology

Shree Bankey Bihari Dental College and Research Centre, Ghaziabad, Uttar Pradesh, India

Vijay Pal Singh, Post-graduate Student, Department of Orthodontics and Dentofacial Orthopaedics

Shree Bankey
Bihari Dental College and Research Centre, Ghaziabad, Uttar Pradesh, India

Krishna Deo Prasad, Professor and Head, Department of Oral & Maxillofacial Pathology and Microbiology

Shree Bankey Bihari Dental College and Research Centre, Ghaziabad, Uttar Pradesh, India

Jalaj Tak, Reader,Department of Oral & Maxillofacial Pathology and Microbiology

Shree Bankey Bihari Dental College and Research Centre, Ghaziabad, Uttar Pradesh, India

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